PKU patients can lead a normal life with Prekulab's nutritional treatment

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Behavioural Effects of Phenylalanine-Free Amino Acid Tablet Supplementation in Intellectually Disabled Adults with Untreated PKU (Part I)

Study made by:

  • Department of Paediatrics, Nutrition & Metabolism Unit, Hacettepe University, Ankara, Turkey
  • The John F. Kennedy Institute, Glostrup, Denmark
  • Department of Statistics, Hacettepe University, Ankara, Turkey

 

 

Behavioural Effects of Phenylalanine-Free Amino Acid Tablet Supplementation in Patients with Untreated PKU (Part II) 

Study made by:

  • Department of Paediatrics, Nutrition & Metabolism Unit, Hacettepe University, Ankara, Turkey
  • The John F. Kennedy Institute, Glostrup, Denmark

 

 

Benefits of Using PreKUnil As Treatment for Adults with PKU In Denmark

Study made by: 

The Department of Neuropaediatrics, J.F. Kennedy Institute, Glostrup, Denmark.

 

 

Brain Phenylalanine Concentrations in PKU: Research and Treatment of Adults (Latest Edition)

Study made by:

  • Rex A. Moats, Ph.D.
  • Kathrine D. Moesley, M.S. R.D
  • Richard Koch, M.D.
  • Marvin Nelson, M.D.

 

 

Classical Treatment Vs. Tyrosine And Tryptophan Supplement in PKU Similar Effects on Plasma Branched Chain Amino Acid Levels

 

Study made by:

  • Troels Kjær
  • Kirsten Ahring, B.S
  • Ingrid Mikkelsen, B.S
  • Maria Jose Miranda Gimenez-Rico, M.D., Ph.D
  • Flemming Güttler, M.D., Ph.D
  • Hans Lou, M.D., Ph.D

 

 

Cognitive Performance in Adolescent PKU Patients on Relaxed Diet Supplemented with Phenylalanine-Free Amino Acid Tablets Vs. Strict Dietary Therapy (Part I) 

 

Study made by:

  • Jente Andersen, M.Sc
  • Kirsten Ahring, B.S
  • Ingrid Mikkelsen, B.S
  • Maria Jose Miranda Gimenez-Rico, M.D., Ph.D
  • Flemming Güttler, M.D., Ph.D
  • Hans Lou, M.D., Ph.D

 

 

Cognitive Performance in Adolescent PKU Patients on Relaxed Diet Supplemented with Phenylalanine-Free Amino Acid Tablets Vs. Strict Dietary Therapy (Part II) 

Study made by:

  • Jente Andresen, M.Sc
  • Kirsten Ahring, B.S
  • Ingrid Mikkelsen, B.S
  • Maria Jose Miranda Gimenez-Rico, M.D., Ph.D
  • Flemming Güttler, M.D., Ph.D.
  • Hans Lou, MD, Ph.D.

 

 

Diet With Large Neutral Amino Acids Supplementation
As A Combined Treatment For Difficult To Control Or Late Diagnosed Patients with PKU – Preliminary Data
 

Study made by:

  • M.Gizewska
  • L. Cyrylowski
  • I. Józwiak
  • W. Bich
  • H. Romanowska
  • M. Remigolska
  • A. Bilar
  • E. Bartkowiak
  • M. Walczak

 

 

Effects of Diet Discontinuation and Dietary Tryptophan Supplementation on Neurotransmitter Metabolism in Phenylketonuria 

Study made by:

  • Jytte Beiber Nielsen
  • Hans Lou
  • Flemming Güttler

At The John F. Kennedy Institute, Glostrup, Denmark

 

 

Effects of Dietary mixtures of Amino Acids on fetal growth and maternal and fetal amino acid pools in experimental  maternal Phenylketonuria

Study made by:

  • Richard E Austic
  • Chun-Li Su
  • Barbara J Strupp
  • David A Levitsky

 

 

Effects of LNAA On Blood PHE In PKU

Study made by:

  • University of Texas Medical Branch, Galveston, USA
  • University of Houston, Houston, Texas, USA
  • Kennedy Institute 3, Glostrup, Denmark
  • University of Moscow, Russia
  • Centre for Genetics, Kharkiv, Ukraine

 

 

Future Role of Large Neutral Amino Acids in Transport of Phenylalanine Into the Brain First Edition

Study made by:

  • Reuben Matalon M.D., Ph.D
  • Sankar Surendran, Ph.D
  • Kimberlee Michals Matalon, Ph.D., R.D
  • Stephen Tyring, M.D., Ph.D
  • Michael Quast, Ph.D
  • Wei Jinga, Ph.D
  • Edward Ezell, Ph.D
  • Sylvia Szucs, MS

 

 

Future Role of Large Neutral Amino Acids in Transport of Phenylalanine Into the Brain Latest Edition

Study made by:

  • Reuben Matalon M.D., Ph.D
  • Sankar Surendran, Ph.D
  • Kimberlee Michals Matalon, Ph.D., R.D
  • Stephen Tyring, M.D., Ph.D
  • Michael Quast, Ph.D
  • Wei Jinga, Ph.D
  • Edward Ezell, Ph.D
  • Sylvia Szucs, MS

 

 

Increased Neurotransmitter Biosynthesis in Phenylketonuria Induced by Phenylalanine Restriction or By Supplementation of Unrestricted Diet with Large Amounts of Tyrosine

Study made by:

  • C. Lykkelund
  • J. B. Nielsen
  • H. C. Lou
  • V. Rasmussen
  • A.M. Gerdes
  • E. Christensen
  • F. Güttler

 

 

Increased Tolenrance Of Phenylalanine In The Treatment Of Phenylketonuria With The Use Of Large Neutral Amino Acids

Study made by:

  • K. Moseley
  • M.D. Brawn
  • S. Yano
  • R. Koch

 

 

Increased Vigilance and Dopamine Synthesis by Large Doses of Tyrosine or Phenylalanine Restriction in Phenylketonuria

Study made by:

  • C. Lykkelund
  • H. Udesen
  • H. C. Lou
  • P. Bruhn
  • A.M. Gerdes

 

 

Large Neutral Amino Acids Block Phenylalanine Transport Into Brain Tissue In Patients With Phenylketonuria

Study made by:

  • Joachim Pietz
  • Roland Kreis
  • André Rupp
  • Ertan Mayatepek
  • Chris Boesch
  • Hans Joachim Bremer

 

 

Large Neutral Amino Acids in The Treatment of PKU

Study made by:

  • R. Matalon
  • K. Michals-Matalon
  • G. Bhatia
  • E. Grechanina
  • P. Novikov
  • D. J. McDonald
  • J. Grady
  • S.K. Tyring
  • F. Güttler

 

 

The Effect Of Neurotransmitter Precursors As a Substitute for a Strict Diet In Adolescent PKU Patients

Study made by:

  • Jente Andersen
  • Maria Miranda
  • Hans Lou
  • Department of Neuropaediatrics, J.F. Kennedy Institute, Glostrup, Denmark.